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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease amyloidosis
Comorbidity C0268407|cardiac amyloidosis
Sentences 2
PubMedID- 26453570 Technetium pyrophosphate (99mtc-pyp) scintigraphy is a simple and widely available radiotracer useful to differentiate transthyretin from light-chain amyloidosis in patients with advanced cardiac amyloidosis.
PubMedID- 22017778 Cardiac amyloidosis, the primary determinant of prognosis in systemic amyloidoses, is characterized by infiltration of myocardium by amyloid protein resulting in cardiomyopathy and conduction disturbances.

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